A Rare Case of Extra Gigantic Digit of Sole
نویسندگان
چکیده
The classification of ulnar polydactyly exists of either two or three types. The two-stage classification according to Temtamy and McKusick involves type A and B. In type A there is an extra little finger at the metacarpophalangeal Joint, or more proximal including the carpometacarpal joint. The little finger can be hypoplastic or fully developed. Type B varies from a nubbin to an extra, non-functional little finger part on a pedicle. According to the three-type classification, type I includes nubbins or floating little fingers, type II includes duplications at the MCPJ, and type III includes duplications of the entire ray.1 We report a rare case of extra gigantic digit of sole in a boy. He was initially seen at age of 3 months when the parents brought him to us with complaints of an extra growth on right foot which was growing in size along with general growth of the baby. The peculiar thumb like appearance though on the ulnar aspect of foot was striking. Parents were concerned about the growth of the digit and more importantly they were concerned about the future walking of the child. The baby was checked for any other congenital anomalies by pediatric team and anomaly screening was negative. It was decided to operate on the child at about 6 months of age. This was decided so that the developmental milestone of walking which is usually between 9 months to 1 year is not affected. Radiological imaging showed the extra digit to have a well formed metatarsal bone and rudimentary phalanges. Surgical excision of the extra digit was undertaken and filleting of skin flap of extra digit was used to close the defect. Bone was disarticulated from the bifurcation of metatarsal joint. At present the child has started to stand with support at age of 9 months and has begun to take some baby steps to the delight of the parents. Much of the initial growth and patterning of limbs occurs during weeks 4-8. Limb buds appear at about 4 weeks and much of the basic structures of the limbs (bones and muscle groups) are established by 8 weeks. After 8 weeks, the limb elements then just increase in size. Disruption of growth and/or patterning can result in many possible defects. Polydactyly: extra digits (disruption –usually upregulation– of Shh pathway).2,3 This rare case is reported for gigantic ulnar polydactyly for 2 reasons. The first is the gigantic size of the digit with peculiar thumb like appearance and second to highlight the importance of excision of the digit at right age before the child takes the first baby steps that can be added to the literature. Sanjeevani Hospital, Bangalore, India
منابع مشابه
Extra-axial medulloblastoma in cerebello-pontine angle: A report of a rare case with literature review
Medulloblastoma is quite uncommon in the adult population and even rarer in extra-axial site in cerebello- pontine (CP) angle. In this report, a 23-year-old male patient with a two month history of deafness, nausea, vomiting and ataxia is presented. Clinical and radiological findings demonstrated a heterogeneously enhanced extra-axial lesion in the right CP angle. Total excision was perform...
متن کاملSyndactyly and polydactyly in a mixed-breed dog
Polydactyly is the congenital presence of one or more extra digits. The extra digit often does not contain a full complement of bones. Unilateral syndactyly and polydactyl mixed-breed dog was used as a case study. A three-month old unvaccinated intact female mixed breed dog weighing 8 kg, presented with a deformity of the left forepaw was used for this study. The deformity had been present sinc...
متن کاملConcurrence of Primary Cutaneous Extra Mammary Paget’s Disease and Squamous Cell Carcinoma in situ of Vulva: A Case Report
Extramammary Paget’s disease and vulvar intraepithelial neoplasia are common lesions of vulve, but synchronous occurrence is rare in a same location. Herein we describe a concurrence of primary cutaneous extra mammary Paget’s disease and squamous cell carcinoma in situ of vulva in an Iranian women. A 59 year old woman, initially presented to Kosar teaching hospital gynecology clinic April 2017 ...
متن کاملInfraorbital Tuberculosis: A Case Report
Introduction: Extra-pulmonary tuberculosis (EPTB) arising in extra-oral region in head and neck are rare, and when swellings arise from other sites such as infraorbital region, cheek, etc, tuberculosis is not usually considered for the differential diagnosis (DD) and often the diagnosis is missed and appropriate treatment is delayed. Case Report: We report a rare entity of pri...
متن کامل